| The MTERF family proteins: mitochondrial transcription regulators and beyond M Roberti, PL Polosa, F Bruni, C Manzari, S Deceglie, MN Gadaleta, ... Biochimica et Biophysica Acta (BBA)-Bioenergetics 1787 (5), 303-311, 2009 | 177 | 2009 |
| The GABA transaminase, ABAT, is essential for mitochondrial nucleoside metabolism A Besse, P Wu, F Bruni, T Donti, BH Graham, WJ Craigen, R McFarland, ... Cell metabolism 21 (3), 417-427, 2015 | 154 | 2015 |
| Defective i6A37 Modification of Mitochondrial and Cytosolic tRNAs Results from Pathogenic Mutations in TRIT1 and Its Substrate tRNA JW Yarham, TN Lamichhane, A Pyle, S Mattijssen, E Baruffini, F Bruni, ... PLoS genetics 10 (6), e1004424, 2014 | 132 | 2014 |
| DmTTF, a novel mitochondrial transcription termination factor that recognises two sequences of Drosophila melanogaster mitochondrial DNA M Roberti, PL Polosa, F Bruni, C Musicco, MN Gadaleta, P Cantatore Nucleic Acids Research 31 (6), 1597-1604, 2003 | 110 | 2003 |
| Nuclear Respiratory Factor 2 Induces the Expression of Many but Not All Human Proteins Acting in Mitochondrial DNA Transcription and Replication 2 F Bruni, PL Polosa, MN Gadaleta, P Cantatore, M Roberti Journal of biological chemistry 285 (6), 3939-3948, 2010 | 86 | 2010 |
| A human mitochondrial poly (A) polymerase mutation reveals the complexities of post-transcriptional mitochondrial gene expression WC Wilson, HT Hornig-Do, F Bruni, JH Chang, AA Jourdain, JC Martinou, ... Human molecular genetics 23 (23), 6345-6355, 2014 | 82 | 2014 |
| MTERF3, the most conserved member of the mTERF-family, is a modular factor involved in mitochondrial protein synthesis M Roberti, F Bruni, PL Polosa, C Manzari, MN Gadaleta, P Cantatore Biochimica et Biophysica Acta (BBA)-Bioenergetics 1757 (9-10), 1199-1206, 2006 | 68 | 2006 |
| REXO2 is an oligoribonuclease active in human mitochondria F Bruni, P Gramegna, JMA Oliveira, RN Lightowlers, ... PloS one 8 (5), e64670, 2013 | 66 | 2013 |
| The Drosophila termination factor DmTTF regulates in vivo mitochondrial transcription M Roberti, F Bruni, PL Polosa, MN Gadaleta, P Cantatore Nucleic acids research 34 (7), 2109-2116, 2006 | 59 | 2006 |
| MTERF factors: a multifunction protein family M Roberti, PL Polosa, F Bruni, S Deceglie, MN Gadaleta, P Cantatore Walter de Gruyter 1 (2), 215-224, 2010 | 38 | 2010 |
| Mutations in glycyl-tRNA synthetase impair mitochondrial metabolism in neurons V Boczonadi, K Meyer, H Gonczarowska-Jorge, H Griffin, A Roos, ... Human Molecular Genetics 27 (12), 2187-2204, 2018 | 33 | 2018 |
| In vitro transcription termination activity of the Drosophila mitochondrial DNA-binding protein DmTTF M Roberti, P Fernandez-Silva, PL Polosa, E Fernandez-Vizarra, F Bruni, ... Biochemical and biophysical research communications 331 (1), 357-362, 2005 | 33 | 2005 |
| Confirming TDP2 mutation in spinocerebellar ataxia autosomal recessive 23 (SCAR23) G Zagnoli-Vieira, F Bruni, K Thompson, L He, S Walker, APM de Brouwer, ... Neurology: Genetics 4 (4), e262, 2018 | 29 | 2018 |
| Human mitochondrial nucleases F Bruni, RN Lightowlers, ZM Chrzanowska‐Lightowlers The FEBS journal 284 (12), 1767-1777, 2017 | 29 | 2017 |
| Clinical, biochemical, and genetic features associated with VARS2‐related mitochondrial disease F Bruni, I Di Meo, E Bellacchio, BD Webb, R McFarland, ... Human mutation 39 (4), 563-578, 2018 | 24 | 2018 |
| D-MTERF5 is a novel factor modulating transcription in Drosophila mitochondria F Bruni, C Manzari, M Filice, PL Polosa, M Colella, C Carmone, ... Mitochondrion 12 (5), 492-499, 2012 | 23 | 2012 |
| The Drosophila nuclear factor DREF positively regulates the expression of the mitochondrial transcription termination factor DmTTF MÁ Fernández-Moreno, F Bruni, C Adán, RH Sierra, PL Polosa, ... Biochemical Journal 418 (2), 453-462, 2009 | 17 | 2009 |
| Messenger RNA delivery to mitoribosomes–hints from a bacterial toxin F Bruni, Y Proctor‐Kent, RN Lightowlers, ZM Chrzanowska‐Lightowlers The FEBS Journal 288 (2), 437-451, 2021 | 13 | 2021 |
| Neuroimaging spectrum of inherited neurotransmitter disorders YT Lim, K Mankad, M Kinali, AP Tan Neuropediatrics 51 (01), 006-021, 2020 | 12 | 2020 |
| The mystery of mitochondrial RNases F Bruni, P Gramegna, RN Lightowlers, ZMA Chrzanowska-Lightowlers Biochemical Society Transactions 40 (4), 865-869, 2012 | 11 | 2012 |
Robert W TaylorNewcastle UniversityVerified email at ncl.ac.uk
