| α-Synuclein and ALPS motifs are membrane curvature sensors whose contrasting chemistry mediates selective vesicle binding IM Pranke, V Morello, J Bigay, K Gibson, JM Verbavatz, B Antonny, ... Journal of Cell Biology 194 (1), 89-103, 2011 | 225 | 2011 |
| Correction of CFTR function in nasal epithelial cells from cystic fibrosis patients predicts improvement of respiratory function by CFTR modulators IM Pranke, A Hatton, J Simonin, JP Jais, F Le Pimpec-Barthes, A Carsin, ... Scientific reports 7 (1), 7375, 2017 | 150 | 2017 |
| Emerging therapeutic approaches for cystic fibrosis. From gene editing to personalized medicine I Pranke, A Golec, A Hinzpeter, A Edelman, I Sermet-Gaudelus Frontiers in pharmacology 10, 428647, 2019 | 131 | 2019 |
| Airway surface liquid acidification initiates host defense abnormalities in Cystic Fibrosis J Simonin, E Bille, G Crambert, S Noel, E Dreano, A Edwards, A Hatton, ... Scientific reports 9 (1), 6516, 2019 | 85 | 2019 |
| Biosynthesis of cystic fibrosis transmembrane conductance regulator IM Pranke, I Sermet-Gaudelus The international journal of biochemistry & cell biology 52, 26-38, 2014 | 69 | 2014 |
| Factors influencing readthrough therapy for frequent cystic fibrosis premature termination codons I Pranke, L Bidou, N Martin, S Blanchet, A Hatton, S Karri, D Cornu, ... ERJ open research 4 (1), 2018 | 53 | 2018 |
| Pharmacological chaperones improve intra-domain stability and inter-domain assembly via distinct binding sites to rescue misfolded CFTR N Baatallah, A Elbahnsi, JP Mornon, B Chevalier, I Pranke, N Servel, ... Cellular and Molecular Life Sciences 78, 7813-7829, 2021 | 46 | 2021 |
| Modulators of CFTR. Updates on clinical development and future directions E Bardin, A Pastor, M Semeraro, A Golec, K Hayes, B Chevalier, F Berhal, ... European journal of medicinal chemistry 213, 113195, 2021 | 46 | 2021 |
| Might brushed nasal cells be a surrogate for CFTR modulator clinical response? I Pranke, A Hatton, A Masson, T Flament, M Le Bourgeois, ... American journal of respiratory and critical care medicine 199 (1), 123-126, 2019 | 45 | 2019 |
| Cis variants identified in F508del complex alleles modulate CFTR channel rescue by small molecules N Baatallah, S Bitam, N Martin, N Servel, B Costes, C Mekki, B Chevalier, ... Human Mutation 39 (4), 506-514, 2018 | 36 | 2018 |
| The suppression of premature termination codons and the repair of splicing mutations in CFTR YS Oren, IM Pranke, B Kerem, I Sermet-Gaudelus Current opinion in pharmacology 34, 125-131, 2017 | 35 | 2017 |
| Cystic fibrosis diagnosis in newborns, children, and adults C Castellani, B Linnane, I Pranke, F Cresta, I Sermet-Gaudelus, ... Seminars in respiratory and critical care medicine 40 (06), 701-714, 2019 | 32 | 2019 |
| Rattlesnake phospholipase A2 increases CFTR-chloride channel current and corrects∆ F508CFTR dysfunction: impact in cystic fibrosis G Faure, N Bakouh, S Lourdel, N Odolczyk, A Premchandar, N Servel, ... Journal of Molecular Biology 428 (14), 2898-2915, 2016 | 26 | 2016 |
| An unexpected effect of TNF-α on F508del-CFTR maturation and function S Bitam, I Pranke, M Hollenhorst, N Servel, C Moquereau, D Tondelier, ... F1000Research 4, 2015 | 25 | 2015 |
| Theratyping cystic fibrosis patients to guide elexacaftor/tezacaftor/ivacaftor out-of-label prescription E Dreano, PR Burgel, A Hatton, N Bouazza, B Chevalier, J Macey, ... European Respiratory Journal 62 (4), 2023 | 21 | 2023 |
| Correlating genotype with phenotype using CFTR‐mediated whole‐cell Cl− currents in human nasal epithelial cells S Noel, N Servel, A Hatton, A Golec, M Rodrat, DRS Ng, H Li, I Pranke, ... The Journal of Physiology 600 (6), 1515-1531, 2022 | 20 | 2022 |
| Sweat chloride testing and nasal potential difference (NPD) are primary outcome parameters in treatment with cystic fibrosis transmembrane conductance regulator (CFTR) modulators I Sermet-Gaudelus, T Nguyen-Khoa, A Hatton, K Hayes, I Pranke Journal of Personalized Medicine 11 (8), 729, 2021 | 13 | 2021 |
| The U UGA C sequence provides a favorable context to ELX-02 induced CFTR readthrough IM Pranke, J Varilh, A Hatton, C Faucon, E Girodon, E Dreano, ... Journal of Cystic Fibrosis 22 (3), 560-563, 2023 | 12 | 2023 |
| Changes in lipid raft proteome upon TNF-α stimulation of cystic fibrosis cells C Chhuon, I Pranke, F Borot, D Tondelier, J Lipecka, J Fritsch, M Chanson, ... Journal of proteomics 145, 246-253, 2016 | 10 | 2016 |
| New insights into structure and function of bis-phosphinic acid derivatives and implications for CFTR modulation S Bitam, A Elbahnsi, G Creste, I Pranke, B Chevalier, F Berhal, ... Scientific reports 11 (1), 6842, 2021 | 9 | 2021 |
