Barrington Burnett
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The polyglutamine neurodegenerative protein ataxin-3 binds polyubiquitylated proteins and has ubiquitin protease activity
B Burnett, F Li, RN Pittman
Human molecular genetics 12 (23), 3195-3205, 2003
Impaired synaptic vesicle release and immaturity of neuromuscular junctions in spinal muscular atrophy mice
L Kong, X Wang, DW Choe, M Polley, BG Burnett, M Bosch-Marcé, ...
Journal of Neuroscience 29 (3), 842-851, 2009
Trichostatin A increases SMN expression and survival in a mouse model of spinal muscular atrophy
AM Avila, BG Burnett, AA Taye, F Gabanella, MA Knight, P Hartenstein, ...
The Journal of clinical investigation 117 (3), 659-671, 2007
Mutations in TRPV4 cause Charcot-Marie-Tooth disease type 2C
G Landouré, AA Zdebik, TL Martinez, BG Burnett, HC Stanescu, H Inada, ...
Nature genetics 42 (2), 170-174, 2010
Regulation of SMN protein stability
BG Burnett, E Munoz, A Tandon, DY Kwon, CJ Sumner, KH Fischbeck
Molecular and cellular biology, 2009
MicroRNA pathways modulate polyglutamine-induced neurodegeneration
J Bilen, N Liu, BG Burnett, RN Pittman, NM Bonini
Molecular cell 24 (1), 157-163, 2006
Research capacity. Enabling the genomic revolution in Africa.
C Rotimi, A Abayomi, A Abimiku, VM Adabayeri, C Adebamowo, ...
Science (New York, NY) 344 (6190), 1346-1348, 2014
The polyglutamine neurodegenerative protein ataxin 3 regulates aggresome formation
BG Burnett, RN Pittman
Proceedings of the National Academy of Sciences 102 (12), 4330-4335, 2005
Sustained improvement of spinal muscular atrophy mice treated with trichostatin A plus nutrition
HL Narver, L Kong, BG Burnett, DW Choe, M Bosch‐Marcé, AA Taye, ...
Annals of neurology 64 (4), 465-470, 2008
Mitochondrial abnormalities in spinal and bulbar muscular atrophy
S Ranganathan, GG Harmison, K Meyertholen, M Pennuto, BG Burnett, ...
Human molecular genetics 18 (1), 27-42, 2009
Akt blocks ligand binding and protects against expanded polyglutamine androgen receptor toxicity
I Palazzolo, BG Burnett, JE Young, PL Brenne, AR La Spada, ...
Human molecular genetics 16 (13), 1593-1603, 2007
Cowchock syndrome is associated with a mutation in apoptosis-inducing factor
C Rinaldi, C Grunseich, IF Sevrioukova, A Schindler, I Horkayne-Szakaly, ...
The American Journal of Human Genetics 91 (6), 1095-1102, 2012
Hereditary Spastic Paraplegia Type 43 (SPG43) is Caused by Mutation in C19orf12
G Landouré, PP Zhu, CM Lourenço, JO Johnson, C Toro, KV Bricceno, ...
Human mutation 34 (10), 1357-1360, 2013
Increasing expression and decreasing degradation of SMN ameliorate the spinal muscular atrophy phenotype in mice
DY Kwon, WW Motley, KH Fischbeck, BG Burnett
Human molecular genetics 20 (18), 3667-3677, 2011
Survival motor neuron protein deficiency impairs myotube formation by altering myogenic gene expression and focal adhesion dynamics
KV Bricceno, T Martinez, E Leikina, S Duguez, TA Partridge, ...
Human molecular genetics 23 (18), 4745-4757, 2014
Non-targeted identification of prions and amyloid-forming proteins from yeast and mammalian cells
D Kryndushkin, N Pripuzova, BG Burnett, F Shewmaker
Journal of Biological Chemistry 288 (38), 27100-27111, 2013
Histone deacetylase inhibition suppresses myogenin-dependent atrogene activation in spinal muscular atrophy mice
KV Bricceno, PJ Sampognaro, JP Van Meerbeke, CJ Sumner, ...
Human molecular genetics 21 (20), 4448-4459, 2012
The E3 ubiquitin ligase mind bomb 1 ubiquitinates and promotes the degradation of survival of motor neuron protein
DY Kwon, M Dimitriadi, B Terzic, C Cable, AC Hart, A Chitnis, ...
Molecular biology of the cell 24 (12), 1863-1871, 2013
The role of the immunoproteasome in interferon-γ-mediated microglial activation
KE Moritz, NM McCormack, MB Abera, C Viollet, YJ Yauger, G Sukumar, ...
Scientific reports 7 (1), 9365, 2017
Expression of expanded polyglutamine targets profilin for degradation and alters actin dynamics
BG Burnett, J Andrews, S Ranganathan, KH Fischbeck, NA Di Prospero
Neurobiology of disease 30 (3), 365-374, 2008
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